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E. Snella · SciRah

Researcher profile · Semantic Scholar

E. Snella

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E. Snella — researcher profile on SciRah

h-index: 15
Works: 38
Citations: 739

Most-cited papers

Derivation of adult canine intestinal organoids for translational research in gastroenterology
L. Chandra, Dana C. Borcherding, D. Kingsbury, Todd Atherly +17 more
2019BMC Biology117 citations Open access
Semantic Scholar
Replacing the Enzyme α-L-Iduronidase at Birth Ameliorates Symptoms in the Brain and Periphery of Dogs with Mucopolysaccharidosis Type I
Ashley Dierenfeld, M. Mcentee, C. Vogler, C. Vite +19 more
2010Science Translational Medicine83 citations Open access
Semantic Scholar
Early versus late treatment of spinal cord compression with long-term intrathecal enzyme replacement therapy in canine mucopolysaccharidosis type I
Patricia I. Dickson, S. Hanson, M. McEntee, C. Vite +14 more
2010Molecular Genetics and Metabolism58 citations Open access
Semantic Scholar
Rescue of dystrophic skeletal muscle by PGC-1α involves restored expression of dystrophin-associated protein complex components and satellite cell signaling.
Katrin Hollinger, D. Gardan‐Salmon, C. Santana, Drance Rice +2 more
2013American Journal of Physiology. Regulatory Integrative and Comparative Physiology56 citations Open access
Semantic Scholar
A Mutation in LTBP2 Causes Congenital Glaucoma in Domestic Cats (Felis catus)
M. Kuehn, K. Lipsett, M. Menotti-Raymond, S. Whitmore +8 more
2016PLoS ONE49 citations Open access
Semantic Scholar
Physiology, Biochemistry and Molecular Biology of the Est-6 Locus in Drosophila melanogaster
R. C. Richmond, K. M. Nielsen, J. P. Brady, E. Snella
199049 citations
Semantic Scholar
Active site mutant transgene confers tolerance to human β-glucuronidase without affecting the phenotype of MPS VII mice
W. Sly, C. Vogler, J. Grubb, Mi Zhou +5 more
2001Proceedings of the National Academy of Sciences of the United States of America40 citations Open access
Semantic Scholar
Differential Transcriptomic Profiles Following Stimulation with Lipopolysaccharide in Intestinal Organoids from Dogs with Inflammatory Bowel Disease and Intestinal Mast Cell Tumor
Dipak Kumar Sahoo, Dana C. Borcherding, L. Chandra, A. Jergens +8 more
2022Cancers37 citations Open access
Semantic Scholar
Novel Engraftment and T Cell Differentiation of Human Hematopoietic Cells in ART−/− IL2RG−/Y SCID Pigs
Adeline N. Boettcher, Yun-Sheng Li, A. Ahrens, M. Kiupel +21 more
2020Frontiers in Immunology33 citations Open access
Semantic Scholar
A zebrafish model of Granulin deficiency reveals essential roles in myeloid cell differentiation
Clyde A. Campbell, O. Fursova, Xiao-Yi Cheng, E. Snella +8 more
2020bioRxiv31 citations Open access
Semantic Scholar
Features of brain MRI in dogs with treated and untreated mucopolysaccharidosis type I.
C. Vite, I. Nestrašil, A. Mlikotic, J. Jens +13 more
2013Comparative medicine30 citations
Semantic Scholar
Missense models [Gustm(E536A)Sly, Gustm(E536Q)Sly, and Gustm(L175F)Sly] of murine mucopolysaccharidosis type VII produced by targeted mutagenesis
S. Tomatsu, K. Orii, C. Vogler, J. Grubb +7 more
2002Proceedings of the National Academy of Sciences of the United States of America24 citations Open access
Semantic Scholar
Production of MPS VII mouse (Gustm(hE540A.mE536A)Sly) doubly tolerant to human and mouse β-glucuronidase
S. Tomatsu, K. Orii, C. Vogler, J. Grubb +8 more
200320 citations
Semantic Scholar
Glycosaminoglycan storage in neuroanatomical regions of mucopolysaccharidosis I dogs following intrathecal recombinant human iduronidase
Agnes H. Chen, C. Vogler, M. Mcentee, S. Hanson +7 more
2011Acta Pathologica, Microbiologica et Immunologica Scandinavica (APMIS)17 citations Open access
Semantic Scholar
Removal of potentially confounding phenotypes from a Siamese-derived feline glaucoma breeding colony.
M. M. Rutz-Mendicino, E. Snella, J. Jens, B. Gandolfi +4 more
2011Comparative medicine16 citations
Semantic Scholar
Central nervous system pathology in preclinical MPS IIIB dogs reveals progressive changes in clinically relevant brain regions
M. Egeland, Marta M. Tarczyluk-Wells, Melissa Asmar, Evan G. Adintori +9 more
2020Scientific Reports15 citations Open access
Semantic Scholar
Production of MPS VII mouse (Gus(tm(hE540A x mE536A)Sly)) doubly tolerant to human and mouse beta-glucuronidase.
S. Tomatsu, K. Orii, C. Vogler, J. Grubb +8 more
2003Human Molecular Genetics14 citations
Semantic Scholar
Nod1-dependent NF-kB activation initiates hematopoietic stem cell specification in response to small Rho GTPases
Xiao-Yi Cheng, Radwa A. Barakat, Giulia Pavani, Masuma K. Usha +10 more
2022bioRxiv13 citations Open access
Semantic Scholar
Tralesinidase Alfa Enzyme Replacement Therapy Prevents Disease Manifestations in a Canine Model of Mucopolysaccharidosis Type IIIB
N. Ellinwood, Bethann N. Valentine, A. Hess, J. Jens +33 more
2022Journal of Pharmacology and Experimental Therapeutics7 citations Open access
Semantic Scholar
Novel engraftment and T cell differentiation of human hematopoietic cells in Art-/- IL2RG-/ SCID pigs
Adeline N. Boettcher, Yun-Sheng Li, A. Ahrens, M. Kiupel +21 more
2019bioRxiv6 citations Open access
Semantic Scholar
Pharmacology of BMN 250 administered via intracerebroventricular infusion once every 2 weeks for twenty-six weeks or longer in a canine model of mucopolysaccharidosis type IIIB
N. Ellinwood, Bethann N. Valentine, A. Hess, J. Jens +23 more
20186 citations
Semantic Scholar
Spontaneous Mutations In LTBP2 Are Associated With Congenital Glaucoma In Cats
M. Kuehn, G. J. McLellan, Alexander Pfleging, E. Snella +1 more
20116 citations
Semantic Scholar
Correction: A Mutation in LTBP2 Causes Congenital Glaucoma in Domestic Cats (Felis catus)
M. Kuehn, K. Lipsett, M. Menotti-Raymond, S. Whitmore +8 more
2016PLoS ONE5 citations Open access
Semantic Scholar
Recombinant NAGLU-IGF2 prevents physical and neurological disease and improves survival in Sanfilippo B syndrome
S. Le, Shih-Hsin Kan, Marie S. Roberts, Joshua T. Dearborn +16 more
2021bioRxiv2 citations Open access
Semantic Scholar
Adult Canine Intestinal Derived Organoids: A Novel In Vitro System for Translational Research in Comparative Gastroenterology
L. Chandra, Dana C. Borcherding, D. Kingsbury, Todd Atherly +17 more
20182 citations Open access
Semantic Scholar
Preliminary findings of a twenty-six week or longer intracerebroventricular infusion study of BMN 250 administered once every 2 weeks in a canine model of mucopolysaccharidosis type IIIB
N. Ellinwood, Bethann N. Valentine, A. Hess, J. Jens +21 more
20172 citations
Semantic Scholar
Novel lysosomal disease in a juvenile golden retriever
Jodi D. Smith, Tyler A. Harm, D. LeVine, S. Christopher +4 more
20181 citations
Semantic Scholar
Initial characterization of a murine model of Sanfilippo syndrome type IIID shows similar pathology to other murine models of Sanfilippo syndrome
Maryam Jamil, E. Snella, S. Le, Shih-Hsin Kan +4 more
20161 citations
Semantic Scholar
Preliminary Characterization of the Genetics and Inheritance of Primary Congenital Glaucoma in a Spontaneous Feline Model
N. Ellinwood, J. Jens, M. Rutz, M. P. Faylon +3 more
20091 citations
Semantic Scholar
Intra-articular AAV9 α-iduronidase gene therapy in mucopolysaccharidosis type I canine model
Shih-Hsin Kan, Hao-Yue Zhang, Jodi D. Smith, E. Snella +7 more
20200 citations
Semantic Scholar
Intra-articular AAV9 α-iduronidase gene therapy in the canine model of mucopolysaccharidosis type I results in rapid synovial and cartilage iduronidase expression, clearance of heparan sulfate, and high serum α-iduronidase levels
Raymond Y. Wang, Shih-Hsin Kan, Hao-Yue Zhang, A. Aminian +5 more
2019Molecular Genetics and Metabolism0 citations
Semantic Scholar
Neuroimaging and neuropathology reveal progressively abnormal white matter and cerebrospinal fluid volume in MPS I dogs
P. Dickson, Steven T. Chen, I. Nestrašil, S. Le +10 more
20180 citations
Semantic Scholar
Twenty-six week or longer intracerebroventricular (ICV) infusion study of BMN 250 administered once every 2 weeks in a canine model of mucopolysaccharidosis type IIIB (MPS IIIB)
N. Ellinwood, Bethann N. Johnson, J. Jens, E. Snella +18 more
20160 citations
Semantic Scholar
Discovery and Use of a Natural Mutation that Results in Severe Combined Immuno Deficiency in Pigs
E. Waide, C. Tuggle, N. Ellinwood, J. Ross +9 more
20130 citations Open access
Semantic Scholar
Genetically Determined Storage of Heparan Sulfate Interacts in GalNAc Transferase Null Mice to Confer and Substantially Accelerated MPS III Phenotype
N. Ellinwood, Eman E. A. Mohammed, E. Snella, Michelle Rutz-Mendicino +2 more
20120 citations
Semantic Scholar
49. Treatment from birth improves the efficacy of intravenous rhIDU in MPS I dogs
Matthew Ellinwood, Ashley Derenfeld, E. Snella, J. Jens +3 more
20090 citations
Semantic Scholar
to human and mouse β-glucuronidase
S. Tomatsu, K. Orii, C. Vogler, J. Grubb +8 more
20060 citations
Semantic Scholar
human and mouse b-glucuronidase
S. Tomatsu, K. Orii, C. Vogler, J. Grubb +9 more
20030 citations
Semantic Scholar

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