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A. E. Frazier · SciRah

Researcher profile · Semantic Scholar

A. E. Frazier

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A. E. Frazier — researcher profile on SciRah

h-index: 30
Works: 64
Citations: 5,108

Most-cited papers

MiD49 and MiD51, new components of the mitochondrial fission machinery
Catherine S. Palmer, Laura D. Osellame, D. Laine, O. Koutsopoulos +2 more
2011EMBO Reports638 citations Open access
Semantic Scholar
Accessory subunits are integral for assembly and function of human mitochondrial complex I
D. Stroud, Elliot E. Surgenor, L. E. Formosa, B. Reljić +8 more
2016Nature545 citations Open access
Semantic Scholar
Mitochondrial presequence translocase: switching between TOM tethering and motor recruitment involves Tim21 and Tim17.
A. Chacińska, Maria I. Lind, A. E. Frazier, Jan Dudek +8 more
2005Cell371 citations Open access
Semantic Scholar
Pam16 has an essential role in the mitochondrial protein import motor
A. E. Frazier, Jan Dudek, B. Guiard, W. Voos +11 more
2004Nature Structural &Molecular Biology218 citations Open access
Semantic Scholar
Mitochondrial energy generation disorders: genes, mechanisms, and clues to pathology
A. E. Frazier, D. Thorburn, A. Compton
2017Journal of Biological Chemistry217 citations Open access
Semantic Scholar
Taz1, an outer mitochondrial membrane protein, affects stability and assembly of inner membrane protein complexes: implications for Barth Syndrome.
Katrin Brandner, David U. Mick, A. E. Frazier, Rebecca D. Taylor +2 more
2005Molecular Biology of the Cell213 citations Open access
Semantic Scholar
A J-protein is an essential subunit of the presequence translocase–associated protein import motor of mitochondria
Kaye N. Truscott, W. Voos, A. E. Frazier, Maria I. Lind +10 more
2003Journal of Cell Biology212 citations Open access
Semantic Scholar
Mitochondrial protein-import machinery: correlating structure with function.
M. Baker, A. E. Frazier, J. Gulbis, Michael T. Ryan
2007Trends in Cell Biology201 citations
Semantic Scholar
The Protein Import Machinery of Mitochondria*
Nils Wiedemann, A. E. Frazier, N. Pfanner
2004Journal of Biological Chemistry191 citations Open access
Semantic Scholar
Mitochondrial translocation contact sites: separation of dynamic and stabilizing elements in formation of a TOM–TIM–preprotein supercomplex
A. Chacińska, P. Rehling, B. Guiard, A. E. Frazier +4 more
2003EMBO Journal164 citations Open access
Semantic Scholar
Mdm38 interacts with ribosomes and is a component of the mitochondrial protein export machinery
A. E. Frazier, Rebecca D. Taylor, David U. Mick, B. Warscheid +5 more
2006Journal of Cell Biology147 citations Open access
Semantic Scholar
Shy1 couples Cox1 translational regulation to cytochrome c oxidase assembly
David U. Mick, K. Wagner, M. van der Laan, A. E. Frazier +5 more
2007EMBO Journal143 citations Open access
Semantic Scholar
ATAD3 gene cluster deletions cause cerebellar dysfunction associated with altered mitochondrial DNA and cholesterol metabolism
Radha Desai, A. E. Frazier, Romina Durigon, H. Patel +32 more
2017Brain : a journal of neurology129 citations Open access
Semantic Scholar
Sengers Syndrome-Associated Mitochondrial Acylglycerol Kinase Is a Subunit of the Human TIM22 Protein Import Complex.
Yi-Lin Kang, D. Stroud, M. Baker, D. D. de Souza +8 more
2017Molecules and Cells127 citations Open access
Semantic Scholar
Mutations in the UQCC1-Interacting Protein, UQCC2, Cause Human Complex III Deficiency Associated with Perturbed Cytochrome b Protein Expression
E. Tucker, Bas F. J. Wanschers, R. Szklarczyk, H. Mountford +14 more
2013PLoS Genetics122 citations Open access
Semantic Scholar
N-Acetylcysteine improves mitochondrial function and ameliorates behavioral deficits in the R6/1 mouse model of Huntington's disease
D. Wright, T. Renoir, Z. M. Smith, A. E. Frazier +5 more
2015Translational Psychiatry120 citations Open access
Semantic Scholar
Mitochondrial morphology and distribution in mammalian cells
A. E. Frazier, Clement Kiu, Diana Stojanovski, N. Hoogenraad +1 more
2006Biological chemistry113 citations
Semantic Scholar
Biochemical analyses of the electron transport chain complexes by spectrophotometry.
A. E. Frazier, D. Thorburn
2012Methods in molecular biology106 citations
Semantic Scholar
COA6 is a mitochondrial complex IV assembly factor critical for biogenesis of mtDNA-encoded COX2.
D. Stroud, M. Maher, Caroline Lindau, F. Vögtle +10 more
2015Human Molecular Genetics105 citations
Semantic Scholar
Inhibition of Bak Activation by VDAC2 Is Dependent on the Bak Transmembrane Anchor*
M. Lazarou, Diana Stojanovski, A. E. Frazier, A. Kotevski +5 more
2010Journal of Biological Chemistry102 citations Open access
Semantic Scholar
Structural and functional requirements for activity of the Tim9-Tim10 complex in mitochondrial protein import.
M. Baker, C. Webb, D. Stroud, Catherine S. Palmer +5 more
2008Molecular Biology of the Cell78 citations Open access
Semantic Scholar
Human Miltons associate with mitochondria and induce microtubule-dependent remodeling of mitochondrial networks.
O. Koutsopoulos, D. Laine, Laura D. Osellame, D. Chudakov +3 more
2010Biochimica et Biophysica Acta76 citations Open access
Semantic Scholar
Characterization of mitochondrial FOXRED1 in the assembly of respiratory chain complex I.
L. E. Formosa, M. Mimaki, A. E. Frazier, M. McKenzie +4 more
2015Human Molecular Genetics75 citations Open access
Semantic Scholar
High-intensity training induces non-stoichiometric changes in the mitochondrial proteome of human skeletal muscle without reorganisation of respiratory chain content
C. Granata, N. Caruana, J. Botella, N. Jamnick +13 more
2021Nature Communications74 citations Open access
Semantic Scholar
Mitochondrial OXA Translocase Plays a Major Role in Biogenesis of Inner-Membrane Proteins
Sebastian B. Stiller, Jan Höpker, S. Oeljeklaus, Conny Schütze +10 more
2016Cell Metabolism70 citations Open access
Semantic Scholar
Mitochondria Use Different Mechanisms for Transport of Multispanning Membrane Proteins through the Intermembrane Space
A. E. Frazier, A. Chacińska, Kaye N. Truscott, B. Guiard +2 more
2003Molecular and Cellular Biology68 citations Open access
Semantic Scholar
Fatal perinatal mitochondrial cardiac failure caused by recurrent de novo duplications in the ATAD3 locus
A. E. Frazier, A. Compton, Yoshihito Kishita, D. Hock +41 more
2020i Medicina60 citations Open access
Semantic Scholar
Function of hTim8a in complex IV assembly in neuronal cells provides insight into pathomechanism underlying Mohr-Tranebjærg syndrome
Yi-Lin Kang, Alexander J. Anderson, Thomas D. Jackson, Catherine S. Palmer +11 more
2019eLife45 citations Open access
Semantic Scholar
Assessment of mitochondrial respiratory chain enzymes in cells and tissues.
A. E. Frazier, Amy E. Vincent, D. Turnbull, D. Thorburn +1 more
2020Methods in Cell Biology40 citations Open access
Semantic Scholar
Inhibition of heme biosynthesis triggers cuproptosis in acute myeloid leukemia.
Alexander C. Lewis, Emily Gruber, Rheana L Franich, Jessica Armstrong +26 more
2025Cell30 citations Open access
Semantic Scholar
Mitochondrial biology and dysfunction in secondary mitochondrial disease
Megan J. Baker, Jordan J. Crameri, D. Thorburn, A. E. Frazier +1 more
2022Open Biology30 citations Open access
Semantic Scholar
Functional Characterization of Friedreich Ataxia iPS-Derived Neuronal Progenitors and Their Integration in the Adult Brain
M. Bird, Karina Needham, A. E. Frazier, J. van Rooijen +10 more
2014PLoS ONE29 citations Open access
Semantic Scholar
Sideroflexin 4 is a complex I assembly factor that interacts with the MCIA complex and is required for the assembly of the ND2 module
Thomas D. Jackson, Jordan J. Crameri, Linden S Muellner-Wong, A. E. Frazier +10 more
2022Proceedings of the National Academy of Sciences of the United States of America25 citations Open access
Semantic Scholar
Loss of BIM increases mitochondrial oxygen consumption and lipid oxidation, reduces adiposity and improves insulin sensitivity in mice
Jibran A. Wali, S. Galic, C. Tan, E. N. Gurzov +14 more
2017Cell Death and Differentiation25 citations Open access
Semantic Scholar
The TIM22 complex mediates the import of sideroflexins and is required for efficient mitochondrial one-carbon metabolism
Thomas D. Jackson, D. Hock, Kenji M. Fujihara, Catherine S. Palmer +8 more
2021Molecular Biology of the Cell24 citations Open access
Semantic Scholar
Modelling Mitochondrial Disease in Human Pluripotent Stem Cells: What Have We Learned?
Cameron L. McKnight, Y. C. Low, D. Elliott, D. Thorburn +1 more
2021International Journal of Molecular Sciences23 citations Open access
Semantic Scholar
CLPB disaggregase dysfunction impacts the functional integrity of the proteolytic SPY complex
Megan J. Baker, K. Blau, Alexander J. Anderson, Catherine S. Palmer +7 more
2024Journal of Cell Biology19 citations Open access
Semantic Scholar
Neuronal and astrocyte dysfunction diverges from embryonic fibroblasts in the Ndufs4fky/fky mouse
M. Bird, Xiaonan W. Wijeyeratne, J. Komen, A. Laskowski +3 more
2014Bioscience Reports19 citations Open access
Semantic Scholar
MiD 49 and MiD 51 , novel components of the mitochondrial fission machinery
Catherine S. Palmer, Laura D. Osellame, D. Laine, O. Koutsopoulos +2 more
201119 citations
Semantic Scholar
ATAD 3 gene cluster deletions cause cerebellar dysfunction associated with altered mitochondrial DNA and cholesterol metabolism
Radha Desai, A. E. Frazier, Romina Durigon, H. Patel +32 more
201714 citations
Semantic Scholar
Complex II assembly drives metabolic adaptation to OXPHOS dysfunction
Roopasingam Kugapreethan, S. N. Elahee Doomun, Joanna Sacharz, A. E. Frazier +11 more
2025Science Advances13 citations Open access
Semantic Scholar
Modelling biochemical features of mitochondrial neuropathology.
M. Bird, D. Thorburn, A. E. Frazier
2014Biochimica et Biophysica Acta13 citations
Semantic Scholar
The Australian Genomics Mitochondrial Flagship: A National Program Delivering Mitochondrial Diagnoses
R. Rius, A. Compton, Naomi Baker, S. Balasubramaniam +63 more
2023medRxiv11 citations Open access
Semantic Scholar
Reduced Protein Import via TIM23 SORT Drives Disease Pathology in TIMM50-Associated Mitochondrial Disease
Jordan J. Crameri, Catherine S. Palmer, T. Stait, Thomas D. Jackson +8 more
2024Molecular and Cellular Biology10 citations Open access
Semantic Scholar
Atf3 controls transitioning in female mitochondrial cardiomyopathy as identified by spatial and single-cell transcriptomics
Tasneem Qaqorh, Yusuke Takahashi, Kohei Sameshima, Kentaro Otani +26 more
2025Science Advances9 citations Open access
Semantic Scholar
Deletion of the Complex I Subunit NDUFS4 Adversely Modulates Cellular Differentiation
Jacqueline L Johnson, William Lee, A. E. Frazier, Vijesh Vaghjiani +8 more
2016Stem Cells and Development9 citations Open access
Semantic Scholar
Rothmund-Thomson Syndrome-Like RECQL4 Truncating Mutations Cause a Haploinsufficient Low-Bone-Mass Phenotype in Mice
Wilson Castillo-Tandazo, A. E. Frazier, N. Sims, Monique F. Smeets +1 more
2020Molecular and Cellular Biology8 citations Open access
Semantic Scholar
Multi-omics reveal intricate network of mitochondrial adaptations to training in human skeletal muscle
C. Granata, N. Caruana, J. Botella, N. Jamnick +13 more
20216 citations Open access
Semantic Scholar
Legionella effector LpPIP recruits protein phosphatase 1 to the mitochondria to induce dephosphorylation of outer membrane proteins
K. Yek, Evie R Hodgson, Ching-Seng Ang, Catherine S. Palmer +3 more
2025PLoS Biology3 citations Open access
Semantic Scholar
Mainstreaming proteomics into rare disease diagnostics
D. Hock, A. Compton, S. Amarasekera, A. E. Frazier +9 more
2022Pathology (Sydney)1 citations
Semantic Scholar

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D. Stroud×13
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Diana Stojanovski×10
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Catherine S. Palmer

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