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Hideaki Moteki · SciRah

Researcher profile · Semantic Scholar

Hideaki Moteki

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Hideaki Moteki — researcher profile on SciRah

h-index: 28
Works: 89
Citations: 2,095

Most-cited papers

Towards a Unified Testing Framework for Single-Sided Deafness Studies: A Consensus Paper
P. Van de Heyning, D. Tȧvora-Vieira, G. Mertens, V. van Rompaey +35 more
2017Audiology and Neurotology181 citations Open access
Semantic Scholar
RNA Interference Prevents Autosomal-Dominant Hearing Loss
S. B. Shibata, Paul T Ranum, Hideaki Moteki, Bifeng Pan +5 more
2016American Journal of Human Genetics119 citations Open access
Semantic Scholar
IgG4-related chronic rhinosinusitis: A new clinical entity of nasal disease
Hideaki Moteki, M. Yasuo, H. Hamano, T. Uehara +1 more
2010Acta Oto-Laryngologica111 citations Open access
Semantic Scholar
Etiology of single-sided deafness and asymmetrical hearing loss
S. Usami, Ryosuke Kitoh, Hideaki Moteki, S. Nishio +6 more
2017Acta Oto-Laryngologica104 citations Open access
Semantic Scholar
Targeted Allele Suppression Prevents Progressive Hearing Loss in the Mature Murine Model of Human TMC1 Deafness.
Hidekane Yoshimura, S. B. Shibata, Paul T Ranum, Hideaki Moteki +1 more
2019Molecular Therapy82 citations Open access
Semantic Scholar
Frequency and clinical features of hearing loss caused by STRC deletions
Yoh Yokota, Hideaki Moteki, S. Nishio, Tomomi Yamaguchi +14 more
2019Scientific Reports76 citations Open access
Semantic Scholar
Achievement of hearing preservation in the presence of an electrode covering the residual hearing region
S. Usami, Hideaki Moteki, N. Suzuki, Hisakuni Fukuoka +5 more
2011Acta Oto-Laryngologica71 citations Open access
Semantic Scholar
Hearing preservation and clinical outcome of 32 consecutive electric acoustic stimulation (EAS) surgeries
S. Usami, Hideaki Moteki, K. Tsukada, Maiko Miyagawa +8 more
2014Acta Oto-Laryngologica66 citations Open access
Semantic Scholar
Clinical profile of hearing loss in children with congenital cytomegalovirus (CMV) infection: CMV DNA diagnosis using preserved umbilical cord
S. Furutate, Satoshi Iwasaki, S. Nishio, Hideaki Moteki +1 more
2011Acta Oto-Laryngologica50 citations Open access
Semantic Scholar
Cochlear Implantation From the Perspective of Genetic Background
S. Usami, S. Nishio, Hideaki Moteki, Maiko Miyagawa +1 more
2020The Anatomical Record49 citations Open access
Semantic Scholar
Long-term results of hearing preservation cochlear implant surgery in patients with residual low frequency hearing
Hideaki Moteki, S. Nishio, Maiko Miyagawa, K. Tsukada +2 more
2017Acta Oto-Laryngologica44 citations
Semantic Scholar
Gene Expression Profiles of the Cochlea and Vestibular Endorgans
S. Nishio, Mitsuru Hattori, Hideaki Moteki, K. Tsukada +8 more
2015Annals of Otology, Rhinology and Laryngology42 citations Open access
Semantic Scholar
Mutations in the MYO15A Gene Are a Significant Cause of Nonsyndromic Hearing Loss
Maiko Miyagawa, S. Nishio, Mitsuru Hattori, Hideaki Moteki +6 more
2015Annals of Otology, Rhinology and Laryngology42 citations
Semantic Scholar
Comprehensive genetic testing with ethnic-specific filtering by allele frequency in a Japanese hearing-loss population
Hideaki Moteki, H. Azaiez, Kevin T. A. Booth, A. Shearer +6 more
2015Clinical Genetics42 citations Open access
Semantic Scholar
WFS1 mutation screening in a large series of Japanese hearing loss patients: Massively parallel DNA sequencing-based analysis
Masafumi Kobayashi, Maiko Miyagawa, S. Nishio, Hideaki Moteki +17 more
2018PLoS ONE41 citations Open access
Semantic Scholar
Comprehensive analysis of syndromic hearing loss patients in Japan
Michie Ideura, S. Nishio, Hideaki Moteki, Y. Takumi +37 more
2019Scientific Reports40 citations Open access
Semantic Scholar
The Patients Associated With TMPRSS3 Mutations Are Good Candidates for Electric Acoustic Stimulation
Maiko Miyagawa, S. Nishio, Yuika Sakurai, Mitsuru Hattori +4 more
2015Annals of Otology, Rhinology and Laryngology38 citations
Semantic Scholar
Patients with CDH23 mutations and the 1555A>G mitochondrial mutation are good candidates for electric acoustic stimulation (EAS)
S. Usami, Maiko Miyagawa, S. Nishio, Hideaki Moteki +4 more
2012Acta Oto-Laryngologica38 citations Open access
Semantic Scholar
POU4F3 mutation screening in Japanese hearing loss patients: Massively parallel DNA sequencing-based analysis identified novel variants associated with autosomal dominant hearing loss
Tomohiro Kitano, Maiko Miyagawa, S. Nishio, Hideaki Moteki +17 more
2017PLoS ONE37 citations Open access
Semantic Scholar
The Prevalence and Clinical Characteristics of TECTA-Associated Autosomal Dominant Hearing Loss
Rika Yasukawa, Hideaki Moteki, S. Nishio, Kotaro Ishikawa +14 more
2019Genes36 citations Open access
Semantic Scholar
An effective screening strategy for deafness in combination with a next-generation sequencing platform: a consecutive analysis
Naoko Sakuma, Hideaki Moteki, Masahiro Takahashi, S. Nishio +4 more
2016Journal of Human Genetics36 citations Open access
Semantic Scholar
Detection and confirmation of deafness-causing copy number variations in the STRC gene by massively parallel sequencing and comparative genomic hybridization
Hideaki Moteki, H. Azaiez, Christina M. Sloan-Heggen, Kevin T. A. Booth +9 more
2016Annals of Otology, Rhinology and Laryngology36 citations Open access
Semantic Scholar
Simple and efficient germline copy number variant visualization method for the Ion AmpliSeq™ custom panel
S. Nishio, Hideaki Moteki, S. Usami
2018Molecular Genetics & Genomic Medicine35 citations Open access
Semantic Scholar
Mutations in LOXHD1 gene cause various types and severities of hearing loss
Kentaro Mori, Hideaki Moteki, Yumiko Kobayashi, H. Azaiez +5 more
2015Annals of Otology, Rhinology and Laryngology35 citations Open access
Semantic Scholar
Prevalence and clinical features of hearing loss caused by EYA4 variants
Jun Shinagawa, Hideaki Moteki, S. Nishio, K. Ohyama +14 more
2020Scientific Reports32 citations Open access
Semantic Scholar
Effects of EAS cochlear implantation surgery on vestibular function
K. Tsukada, Hideaki Moteki, Hisakuni Fukuoka, Satoshi Iwasaki +1 more
2013Acta Oto-Laryngologica31 citations Open access
Semantic Scholar
TECTA mutations in Japanese with mid-frequency hearing loss affected by zona pellucida domain protein secretion
Hideaki Moteki, S. Nishio, Shigenari Hashimoto, Y. Takumi +4 more
2012Journal of Human Genetics31 citations Open access
Semantic Scholar
Language development in Japanese children who receive cochlear implant and/or hearing aid.
Satoshi Iwasaki, S. Nishio, Hideaki Moteki, Y. Takumi +3 more
2012International Journal of Pediatric Otorhinolaryngology31 citations Open access
Semantic Scholar
The effects of cochlear implantation in Japanese single-sided deafness patients: five case reports
Ryosuke Kitoh, Hideaki Moteki, S. Nishio, S. Shinden +4 more
2016Acta Oto-Laryngologica30 citations
Semantic Scholar
Haplotype Analysis of GJB2 Mutations: Founder Effect or Mutational Hot Spot?
Jun Shinagawa, Hideaki Moteki, S. Nishio, Y. Noguchi +1 more
2020Genes29 citations Open access
Semantic Scholar
Mid-Frequency Hearing Loss Is Characteristic Clinical Feature of OTOA-Associated Hearing Loss
K. Sugiyama, Hideaki Moteki, S. Kitajiri, Tomohiro Kitano +11 more
2019Genes27 citations Open access
Semantic Scholar
Hearing loss caused by a P2RX2 mutation identified in a MELAS family with a coexisting mitochondrial 3243AG mutation
Hideaki Moteki, H. Azaiez, Kevin T. A. Booth, Mitsuru Hattori +8 more
2015Annals of Otology, Rhinology and Laryngology27 citations Open access
Semantic Scholar
Gene Expression Profiles of the Cochlea and Vestibular Endorgans: Localization and Function of Genes Causing Deafness
S. Nishio, Mitsuru Hattori, Hideaki Moteki, K. Tsukada +8 more
201526 citations
Semantic Scholar
Correlation Between White Matter Lesions and Intelligence Quotient in Patients With Congenital Cytomegalovirus Infection.
Y. Inaba, M. Motobayashi, Makoto Nishioka, Tomoki Kaneko +9 more
2016Pediatric Neurology25 citations
Semantic Scholar
Experience with the Vibrant Soundbridge RW-Coupler for round window Vibroplasty with tympanosclerosis
Satoshi Iwasaki, Hiroaki Suzuki, Hideaki Moteki, Maiko Miyagawa +2 more
2012Acta Oto-Laryngologica25 citations Open access
Semantic Scholar
A case of Mikulicz's disease complicated by malignant lymphoma: a postmortem histopathological finding.
T. Uehara, S. Ikeda, H. Hamano, S. Kawa +4 more
2012Internal medicine25 citations Open access
Semantic Scholar
Novel ACTG1 mutations in patients identified by massively parallel DNA sequencing cause progressive hearing loss
Hiroki Miyajima, Hideaki Moteki, T. Day, S. Nishio +11 more
2020Scientific Reports24 citations Open access
Semantic Scholar
Genetic testing has the potential to impact hearing preservation following cochlear implantation
Hidekane Yoshimura, Hideaki Moteki, S. Nishio, Hiroki Miyajima +2 more
2020Acta Oto-Laryngologica24 citations Open access
Semantic Scholar
Clinical Characteristics and In Vitro Analysis of MYO6 Variants Causing Late-onset Progressive Hearing Loss
S. Oka, T. Day, S. Nishio, Hideaki Moteki +12 more
2020Genes24 citations Open access
Semantic Scholar
Feasibility of hearing preservation for residual hearing with longer cochlear implant electrodes
Hideaki Moteki, S. Nishio, Maiko Miyagawa, K. Tsukada +2 more
2018Acta Oto-Laryngologica22 citations Open access
Semantic Scholar
Social Health Insurance-Based Simultaneous Screening for 154 Mutations in 19 Deafness Genes Efficiently Identified Causative Mutations in Japanese Hearing Loss Patients
Kentaro Mori, Hideaki Moteki, Maiko Miyagawa, S. Nishio +1 more
2016PLoS ONE22 citations Open access
Semantic Scholar
De novo mutation in X-linked hearing loss-associated POU3F4 in a sporadic case of congenital hearing loss
Hideaki Moteki, A. Shearer, Shuji Izumi, Yamato Kubota +6 more
2015Annals of Otology, Rhinology and Laryngology20 citations Open access
Semantic Scholar
The prevalence and clinical features of MYO7A-related hearing loss including DFNA11, DFNB2 and USH1B
Kizuki Watanabe, S. Nishio, S. Usami, T. Kumai +170 more
2024Scientific Reports19 citations Open access
Semantic Scholar
A rational approach to identifying newborns with hearing loss caused by congenital cytomegalovirus infection by dried blood spot screening
Hideaki Moteki, Y. Isaka, Y. Inaba, M. Motobayashi +7 more
2018Acta Oto-Laryngologica19 citations
Semantic Scholar
Novel PTPRQ mutations identified in three congenital hearing loss patients with various types of hearing loss
Naoko Sakuma, Hideaki Moteki, H. Azaiez, Kevin T. A. Booth +10 more
2015Annals of Otology, Rhinology and Laryngology19 citations Open access
Semantic Scholar
Genetic background of candidates for EAS (Electric-Acoustic Stimulation)
S. Usami, Maiko Miyagawa, N. Suzuki, Hideaki Moteki +3 more
201019 citations
Semantic Scholar
Electric-acoustic stimulation with longer electrodes for potential deterioration in low-frequency hearing
Hidekane Yoshimura, Hideaki Moteki, S. Nishio, S. Usami
2020Acta Oto-Laryngologica18 citations Open access
Semantic Scholar
A Comparative Analysis of Genetic Hearing Loss Phenotypes in European/American and Japanese Populations
W. D. Walls, Hideaki Moteki, Taylor R. Thomas, S. Nishio +17 more
2020Human Genetics17 citations Open access
Semantic Scholar
Significant pericardial involvement of immunoglobulin G4-related disease.
Takehiro Morita, A. Izawa, H. Hamano, N. Asano +6 more
2014Annals of Thoracic Surgery17 citations
Semantic Scholar
Silicone impression material foreign body in the middle ear: Two case reports and literature review.
N. Suzuki, K. Okamura, Takuya Yano, Hideaki Moteki +3 more
2015Auris, nasus, larynx15 citations
Semantic Scholar

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S. Usami — researcher profile on SciRah
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Satoshi Iwasaki×16
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Y. Takumi — researcher profile on SciRah

Hidekane Yoshimura×8

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H. Azaiez — researcher profile on SciRah

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