Researcher profile · Semantic Scholar

C. Kielar

h-index: 9
Works: 15
Citations: 629

Most-cited papers

Successive neuron loss in the thalamus and cortex in a mouse model of infantile neuronal ceroid lipofuscinosis.
C. Kielar, Lucy Maddox, Ellen Bible, Charlie C. Pontikis +5 more
2007Neurobiology of Disease177 citations Open access
Semantic Scholar
Molecular correlates of axonal and synaptic pathology in mouse models of Batten disease
C. Kielar, T. Wishart, Alice Palmer, S. Dihanich +7 more
2009Human Molecular Genetics97 citations Open access
Semantic Scholar
Synaptic Changes in the Thalamocortical System of Cathepsin D-Deficient Mice: A Model of Human Congenital Neuronal Ceroid-Lipofuscinosis
S. Partanen, A. Haapanen, C. Kielar, Charlie C. Pontikis +6 more
2008Journal of Neuropathology and Experimental Neurology95 citations
Semantic Scholar
Cerebellar Pathology and Motor Deficits in the Palmitoyl Protein Thioesterase 1-Deficient Mouse
S. Macauley, D. F. Wozniak, C. Kielar, Yun Tan +2 more
2009Experimental Neurology89 citations Open access
Semantic Scholar
Insulin receptor substrate 2 is a negative regulator of memory formation
E. Irvine, L. Drinkwater, K. Radwańska, Hind Al‐Qassab +8 more
2011Learning & memory (Cold Spring Harbor, N.Y.)53 citations Open access
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Progressive thalamocortical neuron loss in Cln5 deficient mice: distinct effects in Finnish variant late infantile NCL
C. von Schantz, C. Kielar, Stine N. Hansen, Charlie C. Pontikis +4 more
2009Neurobiology of Disease48 citations Open access
Semantic Scholar
Temporal Separation of Aggregation and Ubiquitination during Early Inclusion Formation in Transgenic Mice Carrying the Huntington’s Disease Mutation
Belvin Gong, C. Kielar, A. J. Morton
2012PLoS ONE28 citations Open access
Semantic Scholar
Tensor-Based Morphometry and Stereology Reveal Brain Pathology in the Complexin1 Knockout Mouse
C. Kielar, S. Sawiak, Paloma Navarro Negredo, Desmond H. Y. Tse +1 more
2012PLoS ONE25 citations Open access
Semantic Scholar
Anesthetic index--a new approach.
B. Wolfson, C. Kielar, C. Lake, W. D. Hetrick +1 more
1973Anesthesiology13 citations Open access
Semantic Scholar
Early Neurodegeneration in R6/2 Mice Carrying the Huntington’s Disease Mutation with a Super-Expanded CAG Repeat, Despite Normal Lifespan
C. Kielar, A. J. Morton
2018Journal of Huntington's Disease3 citations Open access
Semantic Scholar
Analgesic “Cocktails” for Pneumoencephalography: Ketamine, Diazepam, Alphaprodine, and Droperidol
B. Wolfson, C. Kielar, N. Shenoy, W. D. Hetrick
1973Anesthesia and Analgesia1 citations
Semantic Scholar
UK Cost-Effectiveness Analysis for Management of CMV Disease in Patients Post Allogeneic Stem Cell Transplantation with a Novel Adoptive T Cell Therapy
M. Nuijten, H. Muller, C. Kielar, K. Peggs
20160 citations Open access
Semantic Scholar
Reactive and synaptic changes precede neuronal loss in mouse models of NCL
C. Kielar, T. Gillingwater, J. Tyynelä, M. Sands +1 more
20080 citations
Semantic Scholar
Early and localized astrocytic activation precedes neuronal loss in mouse models of NCL
C. Kielar, T. Gillingwater, Matthew Richard Sands, J. Tyynelä +1 more
20070 citations
Semantic Scholar
Presynaptic reorganization and neuronal loss in the thalamocortical system of mouse models of NCL
C. Kielar, T. Gillingwater, J. Tyynelä, M. Sands +1 more
20070 citations
Semantic Scholar

Charlie C. Pontikis

×3

S. Macauley×3

Noreen A. Alexander×2

W. D. Hetrick×2

Lucy Maddox×1

Ellen Bible×1

M. Griffey×1

M. Wong×1