Skip to content

Home Search Authors Pakistan News Saved

SciRah

SciRah does not host or store research papers. Results come live from free, official scholarly APIs, and every paper links back to its original source.

Data sources

OpenAlex
Semantic Scholar
Crossref
CORE
arXiv
PubMed

Privacy policy Terms of service

B. Appleby · SciRah

Researcher profile · Semantic Scholar

B. Appleby

Share profile

B. Appleby — researcher profile on SciRah

h-index: 36
Works: 136
Citations: 4,459

Most-cited papers

Biomarkers and diagnostic guidelines for sporadic Creutzfeldt-Jakob disease
P. Hermann, B. Appleby, J. Brandel, B. Caughey +15 more
2021Lancet Neurology273 citations Open access
Semantic Scholar
Rapidly progressive Alzheimer's disease features distinct structures of amyloid-β.
M. Cohen, Chae Kim, Tracy Haldiman, M. Elhag +18 more
2015Brain : a journal of neurology191 citations Open access
Semantic Scholar
Utility of the global CDR® plus NACC FTLD rating and development of scoring rules: Data from the ARTFL/LEFFTDS Consortium
Toji Miyagawa, D. Brushaber, J. Syrjanen, W. Kremers +81 more
2020Alzheimer's & Dementia155 citations Open access
Semantic Scholar
Streamlined alpha-synuclein RT-QuIC assay for various biospecimens in Parkinson’s disease and dementia with Lewy bodies
Connor Bargar, Wen Wang, S. Gunzler, A. Lefèvre +11 more
2021Acta Neuropathologica Communications154 citations Open access
Semantic Scholar
Temporal order of clinical and biomarker changes in familial frontotemporal dementia
A. Staffaroni, M. Quintana, B. Wendelberger, H. Heuer +100 more
2022Nature Medicine145 citations Open access
Semantic Scholar
Prion seeding activity and infectivity in skin samples from patients with sporadic Creutzfeldt-Jakob disease
C. Orrú, Jue Yuan, B. Appleby, Bai-Ya Li +19 more
2017Science Translational Medicine128 citations Open access
Semantic Scholar
Diagnosis of prion diseases by RT-QuIC results in improved surveillance
D. Rhoads, A. Wrona, Aaron Foutz, Janis E. Blevins +8 more
2020Neurology99 citations Open access
Semantic Scholar
Proposed research criteria for prodromal behavioural variant frontotemporal dementia
M. Barker, R. Gottesman, M. Manoochehri, Silvia Chapman +30 more
2022Brain : a journal of neurology93 citations Open access
Semantic Scholar
Iatrogenic Creutzfeldt-Jakob disease with Amyloid-β pathology: an international study
I. Cali, M. Cohen, Stéphane Haїk, Piero Parchi +19 more
2018Acta Neuropathologica Communications88 citations Open access
Semantic Scholar
Genetic screening of a large series of North American sporadic and familial frontotemporal dementia cases
E. Ramos, D. Dokuru, V. V. Van Berlo, Kevin J Wojta +68 more
2020Alzheimer's & Dementia83 citations Open access
Semantic Scholar
Plasma Neurofilament Light for Prediction of Disease Progression in Familial Frontotemporal Lobar Degeneration
Julio C. Rojas, Ping Wang, A. Staffaroni, Carolin Heller +88 more
2021Neurology81 citations Open access
Semantic Scholar
Evaluation of a New Criterion for Detecting Prion Disease With Diffusion Magnetic Resonance Imaging.
A. Bizzi, Riccardo Pascuzzo, Janis E. Blevins, M. Grisoli +9 more
2020JAMA Neurology71 citations Open access
Semantic Scholar
Chronic Wasting Disease in Cervids: Implications for Prion Transmission to Humans and Other Animal Species
M. Osterholm, Cory Anderson, M. Zabel, J. Scheftel +2 more
2019mBio69 citations Open access
Semantic Scholar
Gerstmann-Sträussler-Scheinker disease subtypes efficiently transmit in bank voles as genuine prion diseases
Laura Pirisinu, M. D. Di Bari, C. D'Agostino, Stefano Marcon +8 more
2016Scientific Reports66 citations Open access
Semantic Scholar
Comprehensive cross-sectional and longitudinal analyses of plasma neurofilament light across FTD spectrum disorders
Tania F. Gendron, M. Heckman, L. White, Austin M. Veire +78 more
2022Cell Reports Medicine62 citations Open access
Semantic Scholar
Fatal familial insomnia and sporadic fatal insomnia.
L. Cracco, B. Appleby, P. Gambetti
2018Handbook of Clinical Neurology60 citations
Semantic Scholar
Distinct prion-like strains of amyloid beta implicated in phenotypic diversity of Alzheimer's disease
M. Cohen, B. Appleby, J. Safar
2016Prion60 citations Open access
Semantic Scholar
Identification of novel risk loci and causal insights for sporadic Creutzfeldt-Jakob disease: a genome-wide association study
E. Jones, H. Hummerich, Emmanuelle Viré, J. Uphill +61 more
2020Lancet Neurology59 citations Open access
Semantic Scholar
Early preclinical detection of prions in the skin of prion-infected animals
Ze-Rui Wang, M. Manca, Aaron Foutz, M. Camacho +21 more
2019Nature Communications59 citations Open access
Semantic Scholar
Caregiver burden in atypical dementias: comparing frontotemporal dementia, Creutzfeldt–Jakob disease, and Alzheimer's disease
Alice Uflacker, M. Edmondson, C. Onyike, B. Appleby
2015International Psychogeriatrics52 citations Open access
Semantic Scholar
Subtype Diagnosis of Sporadic Creutzfeldt–Jakob Disease with Diffusion Magnetic Resonance Imaging
A. Bizzi, Riccardo Pascuzzo, Janis E. Blevins, M. Moscatelli +9 more
2020Annals of Neurology46 citations Open access
Semantic Scholar
Assessment of executive function declines in presymptomatic and mildly symptomatic familial frontotemporal dementia: NIH-EXAMINER as a potential clinical trial endpoint
A. Staffaroni, Lynn P. Bajorek, K. Casaletto, Y. Cobigo +88 more
2020Alzheimer's & Dementia45 citations Open access
Semantic Scholar
Clinical and volumetric changes with increasing functional impairment in familial frontotemporal lobar degeneration
Nicholas T. Olney, Elise Ong, S. Goh, Lynn P. Bajorek +83 more
2019Alzheimer's & Dementia44 citations Open access
Semantic Scholar
Phenotypic diversity of genetic Creutzfeldt–Jakob disease: a histo-molecular-based classification
Simone Baiardi, Marcello Rossi, A. Mammana, B. Appleby +15 more
2021Acta Neuropathologica43 citations Open access
Semantic Scholar
Genetic aspects of human prion diseases
B. Appleby, Shashirekha Shetty, Mohamed Elkasaby
2022Frontiers in Neurology40 citations Open access
Semantic Scholar
Individualized atrophy scores predict dementia onset in familial frontotemporal lobar degeneration
A. Staffaroni, Y. Cobigo, S. Goh, J. Kornak +86 more
2020Alzheimer's & Dementia38 citations Open access
Semantic Scholar
Prion disease incidence in the United States: 2003–2015
Ryan A. Maddox, M. Person, Janis E. Blevins, Joseph Y. Abrams +3 more
2019Neurology37 citations
Semantic Scholar
Prion propagation estimated from brain diffusion MRI is subtype dependent in sporadic Creutzfeldt–Jakob disease
Riccardo Pascuzzo, N. Oxtoby, A. Young, Janis E. Blevins +8 more
2020Acta Neuropathologica35 citations Open access
Semantic Scholar
Variably protease-sensitive prionopathy.
S. Notari, B. Appleby, P. Gambetti
2018Handbook of Clinical Neurology33 citations
Semantic Scholar
Clinical Laboratory Tests Used To Aid in Diagnosis of Human Prion Disease
Allyson Connor, Han Wang, B. Appleby, D. Rhoads
2019Journal of Clinical Microbiology32 citations Open access
Semantic Scholar
Nonlinear Z-score modeling for improved detection of cognitive abnormality
J. Kornak, J. Fields, W. Kremers, Sarah Farmer +89 more
2019Alzheimer's & Dementia28 citations Open access
Semantic Scholar
Fluorodeoxyglucose Positron Emission Tomography (FDG-PET) Correlation of Histopathology and MRI in Prion Disease
Karin Mente, J. O'Donnell, Stephen E. Jones, M. Cohen +5 more
2017Alzheimer Disease and Associated Disorders27 citations Open access
Semantic Scholar
Clinical Use of Improved Diagnostic Testing for Detection of Prion Disease
M. Figgie, B. Appleby
2021Viruses26 citations Open access
Semantic Scholar
Rapidly Progressive Alzheimer’s Disease in Two Distinct Autopsy Cohorts
Jagan A. Pillai, B. Appleby, J. Safar, J. Leverenz
2018Journal of Alzheimer's Disease26 citations Open access
Semantic Scholar
Co-existence of PrPD types 1 and 2 in sporadic Creutzfeldt-Jakob disease of the VV subgroup: phenotypic and prion protein characteristics
I. Cali, G. Puoti, J. Smucny, P. Curtiss +6 more
2020Scientific Reports24 citations Open access
Semantic Scholar
Shortening heparan sulfate chains prolongs survival and reduces parenchymal plaques in prion disease caused by mobile, ADAM10-cleaved prions
Patricia Aguilar-Calvo, Alejandro M. Sevillano, Jaidev Bapat, K. Soldau +14 more
2019Acta Neuropathologica23 citations Open access
Semantic Scholar
Feasibility and acceptability of remote smartphone cognitive testing in frontotemporal dementia research
Jack C Taylor, H. Heuer, Annie L. Clark, Amy B. Wise +38 more
2023Alzheimer's & Dementia22 citations Open access
Semantic Scholar
Symptomatic treatment, care, and support of CJD patients.
B. Appleby, Deborah R Yobs
2018Handbook of Clinical Neurology21 citations
Semantic Scholar
Novel strain properties distinguishing sporadic prion diseases sharing prion protein genotype and prion type
L. Cracco, S. Notari, I. Cali, M. Sy +8 more
2017Scientific Reports21 citations Open access
Semantic Scholar
Clinical and imaging characteristics of late onset mitochondrial membrane protein-associated neurodegeneration (MPAN)
Ethan Gore, B. Appleby, M. Cohen, S. Debrosse +5 more
2016Neurocase21 citations Open access
Semantic Scholar
Recognition memory and divergent cognitive profiles in prodromal genetic frontotemporal dementia
M. Barker, M. Manoochehri, Sandra J. Rizer, B. Appleby +30 more
2021Cortex; a journal devoted to the study of the nervous system and behavior20 citations Open access
Semantic Scholar
PMCA-replicated PrPD in urine of vCJD patients maintains infectivity and strain characteristics of brain PrPD: Transmission study
I. Cali, Jody Lavrich, Fabio Moda, Diane Kofskey +6 more
2019Scientific Reports19 citations Open access
Semantic Scholar
A novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease
S. Nemani, Xiangzhu Xiao, I. Cali, L. Cracco +9 more
2020Acta Neuropathologica Communications18 citations Open access
Semantic Scholar
Plasma inflammation for predicting phenotypic conversion and clinical progression of autosomal dominant frontotemporal lobar degeneration
Breton M. Asken, P. Ljubenkov, A. Staffaroni, K. Casaletto +24 more
2023Journal of Neurology Neurosurgery & Psychiatry17 citations Open access
Semantic Scholar
Therapeutic strategies for prion disease: a practical perspective.
B. Appleby, Allyson Connor, Han Wang
2019Current opinion in pharmacology (Print)17 citations
Semantic Scholar
Revised Self-Monitoring Scale
G. Toller, K. Ranasinghe, Y. Cobigo, A. Staffaroni +36 more
2020Neurology16 citations Open access
Semantic Scholar
Rapidly progressive young-onset dementias: neuropsychiatric aspects.
Rajeet Shrestha, Timothy Wuerz, B. Appleby
2015Psychiatric Clinics of North America14 citations
Semantic Scholar
A discriminative event‐based model for subtype diagnosis of sporadic Creutzfeldt‐Jakob disease using brain MRI
V. Venkatraghavan, Riccardo Pascuzzo, E. Bron, M. Moscatelli +8 more
2023Alzheimer's & Dementia13 citations Open access
Semantic Scholar
A young-onset frontal dementia with dramatic calcifications due to a novel CSF1R mutation
Ethan Gore, Andrew T. Manley, D. Dees, B. Appleby +1 more
2016Neurocase13 citations
Semantic Scholar
Human prion diseases
Han Wang, D. Rhoads, B. Appleby
2019Current Opinion in Infectious Diseases12 citations
Semantic Scholar

Frequent co-authors

Invite them to SciRah by sharing their profile.

P. Gambetti×16
Invite
P. Gambetti — researcher profile on SciRah
M. Cohen×15
Invite
M. Cohen — researcher profile on SciRah
J. Kornak×14
Invite
J. Kornak — researcher profile on SciRah
A. Boxer×14
Invite
A. Boxer — researcher profile on SciRah

×14

Invite

N. Ghoshal — researcher profile on SciRah

Invite

E. Huey — researcher profile on SciRah

Invite

I. Litvan — researcher profile on SciRah

B. Dickerson×13

Invite

B. Dickerson — researcher profile on SciRah

K. Domoto-Reilly×13

Invite

K. Domoto-Reilly — researcher profile on SciRah

M. Grossman×13

Invite

M. Grossman — researcher profile on SciRah

D. Brushaber×12

Invite

D. Brushaber — researcher profile on SciRah

M. Tartaglia×12

Invite

M. Tartaglia — researcher profile on SciRah