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P. Niaudet · SciRah

Researcher profile · Semantic Scholar

P. Niaudet

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P. Niaudet — researcher profile on SciRah

h-index: 71
Works: 324
Citations: 19K

Most-cited papers

Genetics and outcome of atypical hemolytic uremic syndrome: a nationwide French series comparing children and adults.
V. Frémeaux-Bacchi, F. Fakhouri, A. Garnier, F. Bienaimé +12 more
2013American Society of Nephrology. Clinical Journal697 citations Open access
Semantic Scholar
Strict blood-pressure control and progression of renal failure in children.
E. Wühl, A. Trivelli, S. Picca, M. Litwin +31 more
2009New England Journal of Medicine630 citations Open access
Semantic Scholar
Acquired and genetic complement abnormalities play a critical role in dense deposit disease and other C3 glomerulopathies.
A. Servais, L. Noël, L. Roumenina, M. Le Quintrec +11 more
2012Kidney International543 citations Open access
Semantic Scholar
Early angiotensin-converting enzyme inhibition in Alport syndrome delays renal failure and improves life expectancy.
O. Gross, C. Licht, H. Anders, B. Hoppe +23 more
2012Kidney International343 citations Open access
Semantic Scholar
KLHL3 mutations cause familial hyperkalemic hypertension by impairing ion transport in the distal nephron
Hélène Louis-dit-Picard, J. Barc, D. Trujillano, S. Miserey-Lenkei +34 more
2012Nature Genetics317 citations Open access
Semantic Scholar
Clinical features of anti-factor H autoantibody-associated hemolytic uremic syndrome.
M. Dragon-Durey, S. Sethi, A. Bagga, C. Blanc +11 more
2010Journal of the American Society of Nephrology294 citations Open access
Semantic Scholar
Eculizumab for Atypical Hemolytic Uremic Syndrome Recurrence in Renal Transplantation
J. Zuber, M. Le Quintrec, S. Krid, C. Bertoye +12 more
2012American Journal of Transplantation277 citations Open access
Semantic Scholar
Eculizumab in severe Shiga-toxin-associated HUS.
Anne-Laure Lapeyraque, M. Malina, V. Frémeaux-Bacchi, T. Boppel +7 more
2011New England Journal of Medicine228 citations Open access
Semantic Scholar
Mutations in the Human Laminin β2 (LAMB2) Gene and the Associated Phenotypic Spectrum
V. Matejas, Bernward G. Hinkes, F. Alkandari, L. Al-Gazali +34 more
2010Human Mutation200 citations Open access
Semantic Scholar
Timing and outcome of renal replacement therapy in patients with congenital malformations of the kidney and urinary tract.
E. Wühl, K. V. van Stralen, E. Verrina, A. Bjerre +9 more
2013American Society of Nephrology. Clinical Journal198 citations Open access
Semantic Scholar
Cysteamine therapy delays the progression of nephropathic cystinosis in late adolescents and adults.
A. Brodin-Sartorius, M. Tête, P. Niaudet, C. Antignac +8 more
2012Kidney International198 citations Open access
Semantic Scholar
Nephropathic cystinosis: an international consensus document.
F. Emma, Galina V. Nesterova, C. Langman, A. Labbé +17 more
2014Nephrology, Dialysis and Transplantation192 citations Open access
Semantic Scholar
Multiple OXPHOS Deficiency in the Liver, Kidney, Heart, and Skeletal Muscle of Patients With Methylmalonic Aciduria and Propionic Aciduria
Y. de Keyzer, V. Valayannopoulos, J. Benoist, F. Batteux +8 more
2009Pediatric Research160 citations
Semantic Scholar
Efficacy and safety of Oxalobacter formigenes to reduce urinary oxalate in primary hyperoxaluria.
B. Hoppe, J. Groothoff, S. Hulton, P. Cochat +5 more
2011Nephrology, Dialysis and Transplantation144 citations Open access
Semantic Scholar
Early-childhood membranous nephropathy due to cationic bovine serum albumin.
H. Dębiec, Florence Lefeu, M. Kemper, P. Niaudet +4 more
2011New England Journal of Medicine139 citations Open access
Semantic Scholar
Genotype-phenotype correlations in non-Finnish congenital nephrotic syndrome.
Eduardo Machuca, G. Benoît, F. Névo, M. Tête +7 more
2010Journal of the American Society of Nephrology138 citations Open access
Semantic Scholar
Overall Neutralization of Complement Factor H by Autoantibodies in the Acute Phase of the Autoimmune Form of Atypical Hemolytic Uremic Syndrome
C. Blanc, L. Roumenina, Y. Ashraf, Satu Hyvärinen +11 more
2012Journal of Immunology113 citations Open access
Semantic Scholar
Lupus Anticoagulant-Hypoprothrombinemia Syndrome: Report of 8 Cases and Review of the Literature
K. Mazodier, L. Arnaud, A. Mathian, N. Costedoat-Chalumeau +11 more
2012Medicine104 citations Open access
Semantic Scholar
Acute kidney injury complicating nephrotic syndrome of minimal change disease.
A. Meyrier, P. Niaudet
2018Kidney International96 citations Open access
Semantic Scholar
Observations of a large Dent disease cohort.
A. Blanchard, E. Curis, Tiphaine Guyon-Roger, Diana Kahila +24 more
2016Kidney International94 citations Open access
Semantic Scholar
Idiopathic Nephrotic Syndrome in Children: Clinical Aspects
P. Niaudet, O. Boyer
201691 citations
Semantic Scholar
A randomized controlled crossover trial with delayed-release cysteamine bitartrate in nephropathic cystinosis: effectiveness on white blood cell cystine levels and comparison of safety.
C. Langman, L. Greenbaum, M. Sarwal, P. Grimm +9 more
2012American Society of Nephrology. Clinical Journal91 citations Open access
Semantic Scholar
Recurrence of nephrotic syndrome after transplantation in a mixed population of children and adults: course of glomerular lesions and value of the Columbia classification of histological variants of focal and segmental glomerulosclerosis (FSGS).
G. Canaud, D. Dion, J. Zuber, M. Gubler +9 more
2010Nephrology, Dialysis and Transplantation90 citations Open access
Semantic Scholar
Mutation Update of the CLCN5 Gene Responsible for Dent Disease 1
L. Mansour-Hendili, A. Blanchard, Nelly Le Pottier, Isabelle Roncelin +64 more
2015Human Mutation85 citations Open access
Semantic Scholar
A randomised Phase I/II trial to evaluate the efficacy and safety of orally administered Oxalobacter formigenes to treat primary hyperoxaluria
B. Hoppe, P. Niaudet, R. Salomon, J. Harambat +7 more
2017Pediatric nephrology (Berlin, West)83 citations
Semantic Scholar
Renal Transplantation Under Prophylactic Eculizumab in Atypical Hemolytic Uremic Syndrome With CFH/CFHR1 Hybrid Protein
S. Krid, LT. Roumenina, D. Beury, M. Charbit +3 more
2012American Journal of Transplantation78 citations Open access
Semantic Scholar
A randomized clinical trial indicates that levamisole increases the time to relapse in children with steroid-sensitive idiopathic nephrotic syndrome.
Mariken Gruppen, A. Bouts, M. C. Jansen-van der Weide, M. Merkus +13 more
2017Kidney International74 citations Open access
Semantic Scholar
Glomerular Lesions in Patients With Sickle Cell Disease
G. Maigné, S. Ferlicot, F. Galactéros, X. Belenfant +9 more
2010Medicine71 citations Open access
Semantic Scholar
Population Pharmacokinetics and Pharmacogenetics of Mycophenolic Acid Following Administration of Mycophenolate Mofetil in De Novo Pediatric Renal‐Transplant Patients
Wei Zhao, M. Fakhoury, G. Deschênes, G. Roussey +9 more
2010Journal of clinical pharmacology70 citations
Semantic Scholar
A new gel formulation of topical cysteamine for the treatment of corneal cystine crystals in cystinosis: the Cystadrops OCT-1 study.
A. Labbé, C. Baudouin, G. Deschênes, C. Loirat +3 more
2014Molecular Genetics and Metabolism61 citations
Semantic Scholar
Hemolytic Uremic Syndrome: New Developments in Pathogenesis and Treatment
O. Boyer, P. Niaudet
2011International Journal of Nephrology61 citations Open access
Semantic Scholar
An international cohort study spanning five decades assessed outcomes of nephropathic cystinosis.
F. Emma, W. Hoff, K. Hohenfellner, R. Topaloğlu +22 more
2021Kidney International60 citations Open access
Semantic Scholar
Mycophenolate mofetil for steroid-dependent nephrotic syndrome: a phase II Bayesian trial
V. Baudouin, C. Alberti, Anne-Laure Lapeyraque, A. Bensman +8 more
2012Pediatric nephrology (Berlin, West)59 citations
Semantic Scholar
Treatment and outcome of congenital nephrotic syndrome
S. Bérody, L. Heidet, O. Gribouval, J. Harambat +26 more
2019Nephrology, Dialysis and Transplantation58 citations
Semantic Scholar
Long-term outcome of children with steroid-sensitive idiopathic nephrotic syndrome.
P. Niaudet
2009American Society of Nephrology. Clinical Journal58 citations Open access
Semantic Scholar
Low levels of urinary epidermal growth factor predict chronic kidney disease progression in children.
K. Ažukaitis, W. Ju, M. Kirchner, V. Nair +112 more
2019Kidney International57 citations Open access
Semantic Scholar
Hydration measurement by bioimpedance spectroscopy and blood pressure management in children on hemodialysis
A. Zaloszyc, Betti Schaefer, F. Schaefer, S. Krid +4 more
2013Pediatric nephrology (Berlin, West)56 citations
Semantic Scholar
Pulse cyclophosphamide therapy and clinical remission in atypical hemolytic uremic syndrome with anti-complement factor H autoantibodies.
O. Boyer, E. Balzamo, M. Charbit, Nathalie Biebuyck-Gougé +4 more
2010American Journal of Kidney Diseases56 citations
Semantic Scholar
Neurological involvement in a child with atypical hemolytic uremic syndrome
B. Koehl, O. Boyer, Nathalie Biebuyck-Gougé, M. Kossorotoff +3 more
2010Pediatric nephrology (Berlin, West)54 citations
Semantic Scholar
Cystinosin is a melanosomal protein that regulates melanin synthesis
C. Chiaverini, L. Sillard, E. Flori, S. Ito +14 more
2012The FASEB Journal53 citations
Semantic Scholar
Non-immunologic mechanisms of calcineurin inhibitors explain its antiproteinuric effects in genetic glomerulopathies
A. Bensman, P. Niaudet
2010Pediatric nephrology (Berlin, West)51 citations Open access
Semantic Scholar
Age-Dependent Risk of Graft Failure in Young Kidney Transplant Recipients
R. Kaboré, C. Couchoud, M. Macher, R. Salomon +13 more
2017Transplantation49 citations
Semantic Scholar
Quality of Life is Improved and Kidney Function Preserved in Patients with Nephropathic Cystinosis Treated for 2 Years with Delayed-Release Cysteamine Bitartrate
C. Langman, L. Greenbaum, P. Grimm, M. Sarwal +10 more
2014Jornal de Pediatria47 citations Open access
Semantic Scholar
Determinants of eGFR at start of renal replacement therapy in paediatric patients.
K. V. van Stralen, E. Tizard, K. Jager, F. Schaefer +14 more
2010Nephrology, Dialysis and Transplantation44 citations Open access
Semantic Scholar
Long‐term results of combined liver‐kidney transplantation for primary hyperoxaluria type 1: The French Experience
P. Compagnon, P. Metzler, D. Samuel, C. Camus +16 more
2014Liver transplantation43 citations Open access
Semantic Scholar
Clinical and genetic heterogeneity in familial steroid-sensitive nephrotic syndrome
G. Dorval, O. Gribouval, Vanesa Martínez-Barquero, Eduardo Machuca +46 more
2018Pediatric nephrology (Berlin, West)41 citations
Semantic Scholar
Clinical features and management of arterial hypertension in children with Williams-Beuren syndrome.
K. Bouchireb, O. Boyer, D. Bonnet, F. Brunelle +5 more
2010Nephrology, Dialysis and Transplantation41 citations
Semantic Scholar
Long-term remission of atypical HUS with anti-factor H antibodies after cyclophosphamide pulses
G. Sana, M. Dragon-Durey, M. Charbit, K. Bouchireb +6 more
2013Pediatric nephrology (Berlin, West)38 citations
Semantic Scholar
Excellent long-term outcome of renal transplantation in cystinosis patients
Camille Cohen, M. Charbit, B. Chadefaux-Vekemans, M. Giral +8 more
2015Orphanet Journal of Rare Diseases34 citations Open access
Semantic Scholar
Allo-immune membranous nephropathy and recombinant aryl sulfatase replacement therapy: a need for tolerance induction therapy.
H. Dębiec, V. Valayannopoulos, O. Boyer, L. Noël +5 more
2014Journal of the American Society of Nephrology33 citations Open access
Semantic Scholar

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