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A. Hermann · SciRah

Researcher profile · Semantic Scholar

A. Hermann

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A. Hermann — researcher profile on SciRah

h-index: 52
Works: 216
Citations: 8,188

Most-cited papers

Nusinersen in adults with 5q spinal muscular atrophy: a non-interventional, multicentre, observational cohort study.
T. Hagenacker, C. Wurster, R. Günther, O. Schreiber-Katz +28 more
2020Lancet Neurology264 citations
Semantic Scholar
Effect of High‐Caloric Nutrition on Survival in Amyotrophic Lateral Sclerosis
A. Ludolph, J. Dorst, J. Dreyhaupt, Jochen H Weishaupt +17 more
2019Annals of Neurology156 citations
Semantic Scholar
Peripheral proinflammatory Th1/Th17 immune cell shift is linked to disease severity in amyotrophic lateral sclerosis
Mengmeng Jin, R. Günther, K. Akgün, A. Hermann +1 more
2020Scientific Reports118 citations Open access
Semantic Scholar
A SARS-CoV-2 neutralizing antibody selected from COVID-19 patients binds to the ACE2-RBD interface and is tolerant to most known RBD mutations
F. Bertoglio, Viola Fühner, Maximilian Ruschig, P. A. Heine +37 more
2021Cell Reports81 citations Open access
Semantic Scholar
Small molecule modulation of a redox-sensitive stress granule protein dissolves stress granules with beneficial outcomes for familial amyotrophic lateral sclerosis models
R. Wheeler, Hyun O. Lee, I. Poser, A. Pal +20 more
2019bioRxiv78 citations Open access
Semantic Scholar
Phenotypes and malignancy risk of different FUS mutations in genetic amyotrophic lateral sclerosis
Marcel Naumann, K. Peikert, R. Günther, A. J. van der Kooi +15 more
2019Annals of Clinical and Translational Neurology72 citations Open access
Semantic Scholar
Ranking Biomarkers of Aging by Citation Profiling and Effort Scoring
A. Hartmann, C. Hartmann, Riccardo Secci, A. Hermann +2 more
2021Frontiers in Genetics70 citations Open access
Semantic Scholar
Informal Caregiving in Amyotrophic Lateral Sclerosis (ALS): A High Caregiver Burden and Drastic Consequences on Caregivers’ Lives
Pavel Schischlevskij, I. Cordts, R. Günther, B. Stolte +24 more
2021Brain Science64 citations Open access
Semantic Scholar
Neurofilament light chain in serum of adolescent and adult SMA patients under treatment with nusinersen
C. Wurster, P. Steinacker, R. Günther, J. Koch +13 more
2019Journal of Neurology64 citations
Semantic Scholar
Knocking out C9ORF72 Exacerbates Axonal Trafficking Defects Associated with Hexanucleotide Repeat Expansion and Reduces Levels of Heat Shock Proteins
Masin Abo-Rady, N. Kalmbach, A. Pal, Carina Schludi +15 more
2020Stem Cell Reports61 citations Open access
Semantic Scholar
Motor Unit Number Index (MUNIX) of hand muscles is a disease biomarker for adult spinal muscular atrophy.
R. Günther, C. Neuwirth, J. Koch, P. Lingor +5 more
2019Clinical Neurophysiology61 citations
Semantic Scholar
Co-condensation of proteins with single- and double-stranded DNA
Roman Renger, J. A. Morin, Regis Lemaitre, Martine Ruer-Gruss +3 more
2021bioRxiv59 citations Open access
Semantic Scholar
Serum creatine kinase and creatinine in adult spinal muscular atrophy under nusinersen treatment
M. Freigang, C. Wurster, T. Hagenacker, B. Stolte +17 more
2021Annals of Clinical and Translational Neurology55 citations Open access
Semantic Scholar
Depending on the stress, histone deacetylase inhibitors act as heat shock protein co-inducers in motor neurons and potentiate arimoclomol, exerting neuroprotection through multiple mechanisms in ALS models
Rachel Kuta, N. Larochelle, M. Fernández, A. Pal +7 more
2020Cell stress & chaperones (Print)52 citations Open access
Semantic Scholar
FUS ALS neurons activate major stress pathways and reduce translation as an early protective mechanism against neurodegeneration.
Barbara Szewczyk, R. Günther, Julia Japtok, M. Frech +3 more
2023Cell Reports50 citations Open access
Semantic Scholar
Altered calcium dynamics and glutamate receptor properties in iPSC derived motor neurons from ALS patients with C9orf72, FUS, SOD1 or TDP43 mutations.
F. Bursch, N. Kalmbach, M. Naujock, Selma Staege +13 more
2019Human Molecular Genetics49 citations
Semantic Scholar
KCNC1‐related disorders: new de novo variants expand the phenotypic spectrum
Joohyun Park, M. Koko, U. Hedrich, A. Hermann +17 more
2019Annals of Clinical and Translational Neurology45 citations Open access
Semantic Scholar
Effect of high-caloric nutrition on serum neurofilament light chain levels in amyotrophic lateral sclerosis
J. Dorst, Joachim Schuster, J. Dreyhaupt, S. Witzel +19 more
2020Journal of Neurology Neurosurgery & Psychiatry43 citations
Semantic Scholar
Therapeutic targeting of Lyn kinase to treat chorea-acanthocytosis
K. Peikert, E. Federti, A. Matte, G. Constantin +33 more
2021Acta Neuropathologica Communications34 citations Open access
Semantic Scholar
Interleukin-17 and Th17 Lymphocytes Directly Impair Motoneuron Survival of Wildtype and FUS-ALS Mutant Human iPSCs
Mengmeng Jin, K. Akgün, T. Ziemssen, M. Kipp +2 more
2021International Journal of Molecular Sciences31 citations Open access
Semantic Scholar
A selectable all-in-one CRISPR prime editing piggyBac transposon allows for highly efficient gene editing in human cell lines
R. Eggenschwiler, Thomas Gschwendtberger, Christian Felski, Christopher Jahn +9 more
2021Scientific Reports30 citations Open access
Semantic Scholar
A Nation-Wide, Multi-Center Study on the Quality of Life of ALS Patients in Germany
Tara Peseschkian, I. Cordts, R. Günther, B. Stolte +25 more
2021Brain Science29 citations Open access
Semantic Scholar
Alteration of Mitochondrial Integrity as Upstream Event in the Pathophysiology of SOD1-ALS
R. Günther, A. Pal, C. Williams, Vitaly L. Zimyanin +12 more
2022Cells28 citations Open access
Semantic Scholar
Impairment of mitochondrial oxidative phosphorylation in skin fibroblasts of SALS and FALS patients is rescued by in vitro treatment with ROS scavengers.
G. Debska-Vielhaber, I. Miller, V. Peeva, W. Zuschratter +10 more
2021Experimental Neurology28 citations
Semantic Scholar
Acanthocyte Sedimentation Rate as a Diagnostic Biomarker for Neuroacanthocytosis Syndromes: Experimental Evidence and Physical Justification
A. Darras, K. Peikert, A. Rabe, F. Yaya +10 more
2021Cells28 citations Open access
Semantic Scholar
TDP‐43 as structure‐based biomarker in amyotrophic lateral sclerosis
L. Beyer, R. Günther, J. Koch, S. Klebe +8 more
2020Annals of Clinical and Translational Neurology28 citations Open access
Semantic Scholar
A 3D cell culture system for bioengineering human neuromuscular junctions to model ALS
Bita Massih, Alexander Veh, M. Schenke, S. Mungwa +8 more
2023Frontiers in Cell and Developmental Biology26 citations Open access
Semantic Scholar
Cognitive reserve and regional brain volume in amyotrophic lateral sclerosis.
Anna G. M. Temp, J. Prudlo, S. Vielhaber, J. Machts +3 more
2021Cortex; a journal devoted to the study of the nervous system and behavior26 citations Open access
Semantic Scholar
Direct Interaction of ATP7B and LC3B Proteins Suggests a Cooperative Role of Copper Transportation and Autophagy
S. Pantoom, Adam Pomorski, K. Huth, C. Hund +4 more
2021Cells26 citations Open access
Semantic Scholar
FUS (fused in sarcoma) is a component of the cellular response to topoisomerase I–induced DNA breakage and transcriptional stress
M. I. Martinez-Macias, D. Moore, R. Green, Fernando Gómez-Herreros +5 more
2019Life Science Alliance26 citations Open access
Semantic Scholar
Assessment of Gene Variant Amenability for Pharmacological Chaperone Therapy with 1-Deoxygalactonojirimycin in Fabry Disease
J. Lukas, Chiara Cimmaruta, L. Liguori, S. Pantoom +7 more
2020International Journal of Molecular Sciences25 citations Open access
Semantic Scholar
The Erythrocyte Sedimentation Rate and Its Relation to Cell Shape and Rigidity of Red Blood Cells from Chorea-Acanthocytosis Patients in an Off-Label Treatment with Dasatinib
A. Rabe, Alexander Kihm, A. Darras, K. Peikert +10 more
2021Biomolecules24 citations Open access
Semantic Scholar
DDX17 is involved in DNA damage repair and modifies FUS toxicity in an RGG-domain dependent manner
Tyler R. Fortuna, Sukhleen Kour, Eric N. Anderson, C. Ward +6 more
2021Acta Neuropathologica24 citations Open access
Semantic Scholar
Routine Cerebrospinal Fluid (CSF) Parameters in Patients With Spinal Muscular Atrophy (SMA) Treated With Nusinersen
C. Wurster, J. Koch, I. Cordts, J. Dreyhaupt +14 more
2019Frontiers in Neurology24 citations Open access
Semantic Scholar
Norepinephrine is a negative regulator of the adult periventricular neural stem cell niche
Grit Weselek, Silke Keiner, M. Fauser, Lisa Wagenführ +7 more
2020Stem Cells23 citations Open access
Semantic Scholar
Proteostasis regulators modulate proteasomal activity and gene expression to attenuate multiple phenotypes in Fabry disease
Susanne Seemann, M. Ernst, Chiara Cimmaruta, S. Struckmann +13 more
2020Biochemical Journal23 citations Open access
Semantic Scholar
Symptomatic pharmacotherapy in ALS: data analysis from a platform-based medication management programme
T. Meyer, D. Kettemann, A. Maier, T. Grehl +14 more
2020Journal of Neurology Neurosurgery & Psychiatry23 citations Open access
Semantic Scholar
Increased chitotriosidase 1 concentration following nusinersen treatment in spinal muscular atrophy
M. Freigang, P. Steinacker, C. Wurster, O. Schreiber-Katz +9 more
2021Orphanet Journal of Rare Diseases20 citations Open access
Semantic Scholar
Pathomechanisms of ALS8: altered autophagy and defective RNA binding protein (RBP) homeostasis due to the VAPB P56S mutation
P. Tripathi, Haihong Guo, A. Dreser, A. Yamoah +15 more
2021Cell Death and Disease20 citations Open access
Semantic Scholar
Patient-Reported Prevalence of Non-motor Symptoms Is Low in Adult Patients Suffering From 5q Spinal Muscular Atrophy
R. Günther, C. Wurster, I. Cordts, J. Koch +7 more
2019Frontiers in Neurology19 citations Open access
Semantic Scholar
MDS criteria for the diagnosis of progressive supranuclear palsy overemphasize Richardson syndrome
Anika Frank, K. Peikert, J. Linn, M. Brandt +1 more
2020Annals of Clinical and Translational Neurology18 citations Open access
Semantic Scholar
Treatment satisfaction in 5q-spinal muscular atrophy under nusinersen therapy
Alma Osmanovic, Gresa Ranxha, Mareike Kumpe, C. Wurster +13 more
2021Therapeutic Advances in Neurological Disorders17 citations Open access
Semantic Scholar
Genome Wide Analysis Points towards Subtype-Specific Diseases in Different Genetic Forms of Amyotrophic Lateral Sclerosis
Banaja P. Dash, Marcel Naumann, J. Sterneckert, A. Hermann
2020International Journal of Molecular Sciences17 citations Open access
Semantic Scholar
Combined Dendritic and Axonal Deterioration Are Responsible for Motoneuronopathy in Patient-Derived Neuronal Cell Models of Chorea-Acanthocytosis
H. Glaß, P. Neumann, A. Pal, Peter Reinhardt +3 more
2020International Journal of Molecular Sciences17 citations Open access
Semantic Scholar
One nerve suffices: A clinically guided nerve ultrasound protocol for the differentiation of multifocal motor neuropathy (MMN) and amyotrophic lateral sclerosis (ALS)
Kai F. Loewenbrück, R. Werner, R. Günther, Markus Dittrich +4 more
2020Journal of Neurology16 citations Open access
Semantic Scholar
A serum microRNA sequence reveals fragile X protein pathology in amyotrophic lateral sclerosis
A. Freischmidt, A. Goswami, Katharina Limm, V. Zimyanin +18 more
2021Brain : a journal of neurology15 citations Open access
Semantic Scholar
Concomitant gain and loss of function pathomechanisms in C9ORF72 amyotrophic lateral sclerosis
A. Pal, Benedikt Kretner, Masin Abo-Rady, Hannes Gla +10 more
2021Life Science Alliance15 citations Open access
Semantic Scholar
Affection of Respiratory Muscles in ALS and SMA
W. Hermann, Simona Langner, M. Freigang, Stefanie Fischer +3 more
2022Journal of Clinical Medicine14 citations Open access
Semantic Scholar
Impact of Organelle Transport Deficits on Mitophagy and Autophagy in Niemann–Pick Disease Type C
Maik Liedtke, Christin Völkner, A. Hermann, M. Frech
2022Cells13 citations Open access
Semantic Scholar
Downstream Effects of Mutations in SOD1 and TARDBP Converge on Gene Expression Impairment in Patient-Derived Motor Neurons
Banaja P. Dash, A. Freischmidt, Jochen H Weishaupt, A. Hermann
2022International Journal of Molecular Sciences12 citations Open access
Semantic Scholar

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