Trilateral retinoblastoma with unilateral eye involvement.
Irfanullah Shaha, Adnan Baig, Abdul Razzaq, Anum Faruqi, Aun Ali, Faraz Qayyum Khan
- aDepartment of Neurosurgery, Chandka Medical College, Larkana. irfanullahshah@ymail.com
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Abstract
Trilateral retinoblastoma (TRb) is a rare combination of unilateral or bilateral retinoblastoma with an ectopic midline intracranial neuroblastic neoplasm (primitive neuroectodermal tumour) usually in the area of pineal gland or sellar region. TRb can occur with both familial and sporadic forms of retinoblastoma. An occurrence of this rare tumour in a 12-year-old boy who had unilateral retinoblastoma in association with ectopic suprasellar primitive neuroectodermal tumour (PNET) is reported here. To the best of our knowledge, this is the first case report in Pakistan on TRb with suprasellar mass.
TL;DRThis is the first case report in Pakistan on TRb with suprasellar mass, which is a rare combination of unilateral or bilateral retinoblastoma with an ectopic midline intracranial neuroblastic neoplasm (primitive neuroectodermal tumour) usually in the area of pineal gland or sellar region. (Semantic Scholar)